Test Code C1Q Complement C1q, Serum
Reporting Name
Complement C1q, SUseful For
Assessment of an undetectable total complement (CH50) level
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Diagnosing congenital C1 (first component of complement) deficiency
Diagnosing acquired deficiency of C1 inhibitor
Performing Laboratory
Mayo Clinic Laboratories in RochesterSpecimen Type
SerumSpecimen Required
Patient Preparation: Fasting for 12 hours
Container/Tube:
Preferred: Red top
Acceptable: Serum gel
Submission Container/Tube: Plastic vial
Specimen Volume: 1 mL
Collection Instructions: Centrifuge and aliquot serum into plastic vial
Specimen Minimum Volume
0.5 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Serum | Refrigerated (preferred) | 28 days | |
Frozen | 28 days | ||
Ambient | 21 days |
Reference Values
12-22 mg/dL
Day(s) Performed
Monday through Friday
Test Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. It has not been cleared or approved by the US Food and Drug Administration.CPT Code Information
86160
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
C1Q | Complement C1q, S | 4478-4 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
C1Q | Complement C1q, S | 4478-4 |
Interpretation
An undetectable C1q in the presence of an absent total complement (CH50) and normal C2, C3, and C4 suggests a congenital C1 (first component of complement) deficiency.
A low C1q in combination with a low C1 inhibitor and low C4 suggests an acquired C1 inhibitor deficiency.
Clinical Reference
1. Stegert M, Bock M, Trendelenburg M: Clinical presentation of human C1q deficiency: How much of a lupus? Mol Immunol. 2015 Sep;67(1):3-11
2. Tangye SG, Al-Herz W, Bousfiha A, et al: Human inborn errors of immunity: 2022 update on the classification from the International Union of Immunological Societies Expert Committee. J Clin Immunol. 2022 Oct;42(7):1473-1507
3. Beurskens FJ, van Schaarenburg RA, Trouw LA: C1q, antibodies and anti-C1q autoantibodies. Mol Immunol. 2015 Nov;68(1):6-13
Report Available
2 to 5 daysMethod Name
Nephelometry